DP09: Blue rubber bleb naevus syndrome: an unusual case of a vascular anomaly presenting with a cutaneous manifestation and underlying gastrointestinal bleeding
نویسندگان
چکیده
منابع مشابه
Blue rubber bleb naevus syndrome.
Blue rubber bleb naevus syndrome (BRBNS) is a rare clinical entity characterised by multiple haemangiomas commonly occurring in the skin and the gastrointestinal (Gl) tract. The association between these cutaneous cavernous haemangiomas and similar lesions in the U l tract was first described in 1860 and the acronym B R B N S was given by Bean in 1958 [ l J, Patients may present with massive GI...
متن کاملExtensive Blue Rubber Bleb Nevus Syndrome with Multiple Gastrointestinal Venous Malformations: A Case Report
Blue rubber bleb nevus syndrome is a sporadic disease with widely distributed dark blue papules and nodules and soft skin-colored compressible protuberances (rubber blebs) as well as large vascular malformations. Gasterointestinal lesions are documented by upper endoscopy and colonoscopy; hemorrhages from these lesions create irondeficinecy anemia. Other sites of visceral involvement are less c...
متن کاملBlue rubber bleb naevus disease: an uncommon cause of gastrointestinal tract bleeding.
A 23 year old woman presented with facial pain, a right parotid tumour and iron deficiency anaemia. She had several cutaneous venous swellings and tumours with a similar appearance were found in the large bowel. Histological examination of the parotid tumour and angiography of the skin and gut lesions confirmed that they were venous in origin. The aetiology, classification, and complications of...
متن کاملSevere gastrointestinal bleeding during pregnancy in a case of blue rubber bleb nevus syndrome.
Blue rubber bleb nevus syndrome (BRBNS) is a rare disorder characterized by distinctive cutaneous and gastrointestinal venous malformations that usually cause massive or occult gastrointestinal hemorrhage and iron deficiency anemia secondary to the bleeding episodes. Only two reports of BRBNS in pregnant women can be found, according to the MEDLINE search. Both cases did not describe severe com...
متن کاملPeriodic exophthalmos associated with the blue rubber bleb naevus syndrome: a case report.
A 71-year-old woman with the blue rubber bleb naevus syndrome experienced 4 episodes of self-limiting unilateral exophthalmos. Is is suggested that a vascular malformation in the orbit is responsible for this phenomenon. A biopsy sample was taken of one of the cutaneous lesions and studied by light and transmission electron microscopy. The histological appearances are discussed in relation to p...
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ژورنال
عنوان ژورنال: British Journal of Dermatology
سال: 2021
ISSN: ['1365-2133', '0007-0963']
DOI: https://doi.org/10.1111/bjd.20261